L’hémoglobinurie paroxystique nocturne est une maladie liée à une mutation somatique entraînant l’expansion de clones cellulaires déficients pour des. Site Internet de la filière de santé maladies rares MaRIH, Publications Aplasie médullaire/Hémoglobinurie paroxystique nocturne/Anémie de Fanconi. Many translated example sentences containing “hémoglobinurie paroxystique nocturne” – English-French dictionary and search engine for English translations.

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Access to the PDF text. Unrelated stem cell transplantation for severe acquired aplastic anemia: Journal page Archives Contents list. The diagnosis is based on flow cytometry, which allowed direct quantification of the GPI-AP-deficient cells. Hematopoietic stem cell transplantation in childhood inherited bone marrow failure syndrome.

A rare disorder characterized by hemolysis and hemoglobinuria, the latter accentuated during sleep. Primary prophylaxis with warfarin prevents thrombosis in paroxysmal nocturnal hemoglobinuria PNH.

Outcome of patients treated The role of antilymphocyte globulin paroxustique the treatment of chronic acquired bone marrow failure. Hematopoietic stem cell transplantation for patients with paroxysmal nocturnal hemoglobinuria previously treated with eculizumab: The disease is diagnosed with haemolytic anemia, marrow failure or episodes of venous thrombosis.

John Libbey Eurotext – Hématologie – Hémoglobinurie paroxystique nocturne

The language you hmoglobiburie must correspond to the language of the term you have entered. If you want to subscribe to this journal, see our rates You can purchase this item in Pay Per View: A study by the severe aplastic anaemia and paediatric disease working parties of the European group blood and bone marrow transplant.


If you are a subscriber, please sign in ‘My Account’ at the top hmoglobinkrie of the screen. Med Sci Paris ; 25 12 You may thus request that your data, should it be inaccurate, incomplete, unclear, outdated, not be used or stored, be corrected, clarified, updated or deleted.

Bluteau O et al. Marchiafava Micheli syndrome Marchiafava-Micheli’s syndrome. Second allogeneic stem cell transplant for aplastic anaemia: FAQ Frequently asked questions Display options. N Engl J Med. Giammarco S et al. Access a collection of Canadian resources on all aspects of English and French, including quizzes.

Alterations in both the hematopoietic microenvironment and the progenitor cell population follow the recovery from myeloablative therapy and bone marrow transplantation.

Publications Aplasie médullaire/Hémoglobinurie paroxystique nocturne/Anémie de Fanconi

Prospective randomized multicenter study comparing cyclosporin alone versus the combination of antithymocyte globulin and cyclosporin for treatment of patients with nonsevere aplastic anemia: Bierings M et al. Gene expression profiling in CD34 cells to identify differences between aplastic anemia patients and healthy volunteers. Granulocyte-stimulating factor and severe aplastic anemia: Personal information regarding our website’s visitors, including their identity, is confidential.


The hematopoietic defect in aplastic anemia assessed by long-term marrow culture. The owners of this website hereby guarantee to respect the legal confidentiality conditions, applicable in France, and not to disclose this data to third parties.

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Recurrent thrombotic events remains even now associated with bad prognosis, whatever the form of the disease. Bacigalupo A et al. Writing tools A collection of writing tools that cover the many facets of English and French grammar, style and usage.

Limited heterogeneity of T cell receptor BV usage in aplastic anemia.

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Evidence for a metabolic shift of arginine metabolism in sickle cell disease. Worse outcome and more chronic GVHD with peripheral blood progenitor cells than bone marrow in HLA-matched sibling donor transplants for young patients with severe acquired aplastic anemia. Optimization of conditioning for marrow transplantation from unrelated donors for patients with aplastic anemia after failure of immunosuppressive therapy. Benajiba L et al.